A fatal combination of duodenal atresia with preduodenal portal vein, malrotation, and hypoplastic left heart syndrome: A case report

Abstract

Background: Duodenal atresia (DA) is often associated with anomalies that include annular pancreas, cardiac anomalies, intestinal malrotation, situs inversus, or splenic anomalies. Association of duodenal atresia with complex cardiac anomalies is scarcely reported in the literature. Case Presentation: A term neonate was diagnosed with duodenal atresia and found to have a preduodenal portal vein and malrotation. A gastro jejunostomy was added to the procedure, due to the pre duodenal portal vein. On post-operative day 4, the patient had sudden desaturation. The respiratory system was normal and there was no evidence of septicaemia. On the post-operative echocardiogram, the diagnosis of hypoplastic left heart was made and the patient eventually succumbed to his complex cardiac disease. Conclusion: This is a rare combination of multiple anomalies and we report the clinical and anatomical findings of this patient.

Keywords

• Duodenal atresia
• Preduodenal portal vein
• Hypoplastic left heart syndrome
• Malrotation