Ceelen-Gellerstedt syndrome in an elderly Indian man: Case report of an unusual case

Abstract

Ceelen-Gellerstedt syndrome, also known as idiopathic pulmonary hemosiderosis (IPH), is a rare disease characterized by recurrent pulmonary alveolar hemorrhages associated with a classical clinical triad of hemoptysis, unexplained iron deficiency anemia, and diffuse pulmonary infiltrates on imaging. We present a case report of Ceelen-Gellerstedt syndrome in an elderly 69-year-old Indian male patient, which is an unusual case as the condition is more common in children and young adults. Diagnosis was suspected on high-resolution computed tomography (HRCT) scan, which revealed diffuse areas of consolidation, ground glass opacities, and septal thickening with perihilar and basal predominance and further workup with bronchoscopy and bronchoalveolar lavage helped to confirm the diagnosis.

Keywords

• Ceelen-Gellerstedt syndrome
• diffuse pulmonary hemorrhage
• hemoptysis
• idiopathic pulmonary hemosiderosis (IPH)
• unexplained iron deficiency anemia