World experience on the treatment of interstitial diseases of the lungs in children (up-date 2017)

Abstract

The article shows modern principles of classification, diagnosis and treatment of interstitial lung diseases in children for the practice of pediatricians, family doctors, pediatric pulmonologists, thoracic surgeons, transplantologists. Interstitial lung diseases are part of the structure of diffuse parenchymal diseases of the lungs, which today includes more than 80 nosological forms. The author presents a chILD (based on evidence base) patient monitoring program, which includes active immunization, treatment of respiratory dysfunction (in its presence), optimal nutrition support, aggressive treatment of intercurrent infection, exclusion of passive smoking and inhalation of other pollutants, education and support, genetic family counseling to the patient, pharmacotherapy and indications for lung transplantation. The publication presents a schedule for patient’s monitoring during the year and a long-term follow-up with the definition of the prediction of a lung disease in a sick child.

Keywords

• children
• lungs
• interstitial
• parenchymal
• diagnosis
• treatment