Urology Case Reports (Nov 2022)

Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract

  • Savannah Starr,
  • Neil Mendhiratta,
  • Paul J. Iskander,
  • Huihui Ye,
  • Renea Sturm

Journal volume & issue
Vol. 45
p. 102218

Abstract

Read online

Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI presents a significant diagnostic challenge due to nonspecific imaging findings and its histologic similarities to alternate benign and malignant entities. Management requires complete local excision and clinical follow-up to monitor for recurrence. Here, we present the diagnosis, management, and two-year follow-up of a 13-month-old boy with a scrotal FHI in addition to a comprehensive literature review of this entity.

Keywords