Frontiers in Medicine (Aug 2021)
Gender Differences in Idiopathic Pulmonary Fibrosis: Are Men and Women Equal?
- Lucile Sesé,
- Lucile Sesé,
- Lucile Sesé,
- Lucile Sesé,
- Hilario Nunes,
- Hilario Nunes,
- Vincent Cottin,
- Dominique Israel-Biet,
- Bruno Crestani,
- Stephanie Guillot-Dudoret,
- Jacques Cadranel,
- Benoit Wallaert,
- Abdellatif Tazi,
- Bernard Maître,
- Gregoire Prévot,
- Sylvain Marchand-Adam,
- Sandrine Hirschi,
- Sandra Dury,
- Violaine Giraud,
- Violaine Giraud,
- Anne Gondouin,
- Philippe Bonniaud,
- Julie Traclet,
- Karine Juvin,
- Raphael Borie,
- Zohra Carton,
- Olivia Freynet,
- Thomas Gille,
- Thomas Gille,
- Carole Planès,
- Carole Planès,
- Dominique Valeyre,
- Dominique Valeyre,
- Yurdagül Uzunhan,
- Yurdagül Uzunhan
Affiliations
- Lucile Sesé
- AP-HP, Service de Physiologie, Hôpital Avicenne, Bobigny, France
- Lucile Sesé
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Lucile Sesé
- EPAR, IPLESP UMR-S 1136, INSERM et Sorbonne Université, Paris, France
- Lucile Sesé
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- Hilario Nunes
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Hilario Nunes
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- Vincent Cottin
- Centre Coordonnateur de Référence des Maladies Pulmonaires Rares, Hôpital Louis Pradel, Hospices Civils de Lyon, Université Lyon 1, Université de Lyon, INRAE, OrphaLung, Member of Respifil, ERN-LUNG, Lyon, France
- Dominique Israel-Biet
- Centre de Compétence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital HEGP, Paris, France
- Bruno Crestani
- Centre Constitutif de Référence des Maladies Pulmonaires Rares AP-HP, Service de Pneumologie, Hôpital Bichat, Paris, France
- Stephanie Guillot-Dudoret
- Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Hôpital Pontchaillou, Rennes, France
- Jacques Cadranel
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Tenon and Sorbonne University, Paris, France
- Benoit Wallaert
- 0Centre Constitutif de Référence des Maladies Pulmonaires Rares, Service de Pneumologie, Hôpital Albert Calmette, Lille, France
- Abdellatif Tazi
- 1Université de Paris, Centre de Référence National des Histiocytoses, AP-HP, Service de Pneumologie, Hôpital Saint-Louis, Paris, France
- Bernard Maître
- 2AP-HP, Service de Pneumologie, Hôpital Henri-Mondor, Créteil, France
- Gregoire Prévot
- 3Service de Pneumologie, Hôpital Larrey, Toulouse, France
- Sylvain Marchand-Adam
- 4Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Hôpital Bretonneau, Tours, France
- Sandrine Hirschi
- 5Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Nouvel Hôpital Civil, Strasbourg, France
- Sandra Dury
- 6Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Hôpital Maison Blanche, Reims, France
- Violaine Giraud
- 5Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Nouvel Hôpital Civil, Strasbourg, France
- Violaine Giraud
- 7AP-HP, Service de Pneumologie, Hôpital Ambroise Paré, Boulogne, France
- Anne Gondouin
- 8Centre de Compétence des Maladies Pulmonaires Rares, Service de Pneumologie, Hôpital Jean Minjoz, Besançon, France
- Philippe Bonniaud
- 9Centre Constitutif de référence des Maladies Pulmonaires Rares, Service de Pneumologie, Centre Hospitalier Universitaire Dijon Bourgogne, Dijon, France
- Julie Traclet
- Centre Coordonnateur de Référence des Maladies Pulmonaires Rares, Hôpital Louis Pradel, Hospices Civils de Lyon, Université Lyon 1, Université de Lyon, INRAE, OrphaLung, Member of Respifil, ERN-LUNG, Lyon, France
- Karine Juvin
- Centre de Compétence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital HEGP, Paris, France
- Raphael Borie
- Centre Constitutif de Référence des Maladies Pulmonaires Rares AP-HP, Service de Pneumologie, Hôpital Bichat, Paris, France
- Zohra Carton
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Olivia Freynet
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Thomas Gille
- AP-HP, Service de Physiologie, Hôpital Avicenne, Bobigny, France
- Thomas Gille
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- Carole Planès
- AP-HP, Service de Physiologie, Hôpital Avicenne, Bobigny, France
- Carole Planès
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- Dominique Valeyre
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Dominique Valeyre
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- Yurdagül Uzunhan
- Centre Constitutif de Référence des Maladies Pulmonaires Rares, AP-HP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
- Yurdagül Uzunhan
- INSERM UMR 1272 “Hypoxia and the Lung,” Université Sorbonne Paris Nord, Bobigny, France
- DOI
- https://doi.org/10.3389/fmed.2021.713698
- Journal volume & issue
-
Vol. 8
Abstract
Background: Idiopathic pulmonary fibrosis (IPF) is characterized by a male predominance. The aim of the study was to explore gender differences in a well-designed French multicentre prospective IPF cohort (COhorte FIbrose, COFI) with a 5-year follow-up.Methods: Between 2007 and 2010, 236 patients with incident IPF were included in COFI. Gender characteristics were compared using a t-test, Chi-squared test and ANOVA, as appropriate. Survival analyses were performed.Results: Fifty-one (22%) females and 185 (78%) males with an average age at diagnosis of 70.1 ± 9.20 and 67.4 ± 10.9 years, respectively, were included in the cohort. Women were significantly less exposed to tobacco smoke [never n = 32 (62.7%) vs. n = 39 (21.1%), p < 0.001] and to occupational exposure [n = 7 (13.7%) vs. n = 63 (34.1%), p = 0.012]. Baseline forced vital capacity, % of predicted (FVC%) was significantly better in women compare to men (83.0% ± 25.0 v. 75.4% ± 18.7 p = 0.046). At presentation honeycombing and emphysema on CT scan were less common in women [n = 40 (78.4%) vs. n = 167 (90.3%) p = 0.041] and [n = 6 (11.8%) vs. n = 48 (25.9%) p = 0.029], respectively. During follow-up fewer women were transplanted compared to men [n = 1 (1.96%) vs. n = 20 (10.8%) p = 0.039]. Medians of survival were comparable by gender [31 months (CI 95%: 28–40) vs. 40 months (CI 95%: 33–72) p = 0.2]. After adjusting for age and FVC at inclusion, being a woman was not associated to a better survival.Conclusions: Women appear to have less advanced disease at diagnosis, maybe due to less exposure history compare to men. Disease progression and overall survival remains comparable regardless gender, but women have less access to lung transplantation.
Keywords