Case Report: Congenital Pulmonary Airway Malformation—A Rare Cystic Lung Malformation

Abstract

Congenital pulmonary airway malformation is a rare congenital malformation of the lower respiratory tract with a worldwide incidence of 1: 11,000 to 1: 33,000 live births. CPAM cases are increasingly being diagnosed antenatally with antenatal anomaly scans having been made compulsory with the availability of improved imaging technologies. Here, we present a case of CPAM in a 14-month-old child who was diagnosed with congenital anomaly during the antenatal scan and was managed with lobectomy to prevent further progression of the disease and preserve the function of normal residual lung parenchyma. Histopathological examination of the lobectomy specimen revealed CPAM type II. During clinical follow-up, the child is asymptomatic and is achieving his developmental goals as per his age.

Keywords

• cpam
• cystic
• malformation