Philippine Journal of Otolaryngology Head and Neck Surgery (Nov 2018)

Congenital Maxillomandibular Fusion: A Rare Case of Isolated True Bony Syngnathia

  • Patrick O. Aguiling,
  • Nikki Lorraine Y. King-Chao,
  • Lyra V. Veloro

DOI
https://doi.org/10.32412/pjohns.v28i2.481
Journal volume & issue
Vol. 28, no. 2

Abstract

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Objective: To present a rare case of congenital maxillomandibular fusion or syngnathia. Methods: Study Design: Case report Setting: Tertiary Private Teaching Hospital Patient: One Results: A 3-year-old girl with oral adhesion (syngnathia) caused by a mandibular to maxillary fibrous band underwent successful surgical division of maxillomandibular bony fusion. Subsequent monitoring and serial oral dilations were performed post operatively, resulting in mouth opening of 24mm over a period of 3 months. Currently, the patient is able to tolerate a general liquid diet. Conclusion: Congenital maxillomandibular fusion is a very rare condition with few cases reported. We hope this report contributes to its diagnosis and management in other children. Keywords: Congenital maxillomandibular fusion, syngnathia

Keywords