Desmoplastic small round cell tumor of the pancreas: An unusual primary site for an uncommon tumor

Abstract

Pancreas is a rare location for desmoplastic small round cell tumor. The present case highlights the dilemma in diagnosis and ascertaining the site of tumor origin. Morphologic and immunohistochemical features were complemented with the molecular markers and tumor origin which was initially nebulous was subsequently confirmed on exploratory laparotomy.

Keywords

• Desmoplastic small round cell tumor
• diagnosis
• molecular pathology
• pancreas