Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome

Mohammad M. Zagzoog, MD; Sean A. Crawford, MD; Thomas Le Houérou, MD; Antoine Gaudin, MD; Stéphan Haulon, MD, PhD; Dominique Fabre, MD, PhD

Journal of Vascular Surgery Cases and Innovative Techniques (Jun 2023)

Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome

Mohammad M. Zagzoog, MD,
Sean A. Crawford, MD,
Thomas Le Houérou, MD,
Antoine Gaudin, MD,
Stéphan Haulon, MD, PhD,
Dominique Fabre, MD, PhD

Affiliations

Mohammad M. Zagzoog, MD: Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France
Sean A. Crawford, MD: Peter Munk Cardiac Centre, Toronto General Hospital, University Health Network, Toronto, ON, Canada
Thomas Le Houérou, MD: Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France
Antoine Gaudin, MD: Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France
Stéphan Haulon, MD, PhD: Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France
Dominique Fabre, MD, PhD: Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France; Correspondence: Dominique Fabre, MD, PhD, Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, 133 Avenue de la Résistance, Le Plessis-Robinson, Paris 92350, France

Journal volume & issue: Vol. 9, no. 2
p. 101156

Abstract

Read online

Vascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented with acute onset of severe sensory deficit of the left leg. Conversion to open repair with a midline laparotomy and an aortic-left popliteal bypass was performed. In the endovascular era, we highlight that even minimally invasive therapeutic interventions can have devastating adverse events in patients with vascular Ehlers-Danlos syndrome.

Published in Journal of Vascular Surgery Cases and Innovative Techniques

ISSN: 2468-4287 (Online)
Publisher: Elsevier
Country of publisher: Netherlands
LCC subjects: Medicine: Surgery; Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.sciencedirect.com/journal/journal-of-vascular-surgery-cases-innovations-and-techniques

About the journal

Abstract

Keywords