Intrathoracic lipoblastoma in a 8 month old infant

Abstract

Lipoblastoma are rare benign tumors of embryonic fat with a tendency to local invasion but not to metastasize. So far, there have been 60 c:ases described in the international literature. There hasn't never been a report in a child older than 8 yr. The main clinical characteristics are the presentation of this tumor which, usually below 3 year of age, the rapid growth of the mass and the peripheral location, mainly in the extremities. In this article, we present our experience with a 8 months-old infant who presented with severe respiratory distress. A chest X-ray showed a total opacity on the right hemithorax, and CT-scan showed a mass that was placed on the right lung mostly in lead upper lobe. thatn was diagnosed as lipoblastoma after pathologic examination of the resected mass. The type of tumor in the our case was right-sided tumor. A complete tumor excision is the best definitive treatment for these tumors. It is important to note that the local recurrence rate of this tumor is 14–25%. Keywords: Lipoblastoma, Intrathoracic, 8 month old infant