Case of Rosai — Dorfman Disease in a Child

Abstract

Sinus histiocytosis with massive lymphadenopathy is rare in children. The article describes a case of Rosai — Dorfman disease in 3-year-old boy. The emergence of lymphadenopathy, mainly cervical one, with synchronous lesion of extranodal area — spleen, enabled to suspect Rosai — Dorfman disease. To clarify the diagnosis, ultrasound has been used. The final diagnosis was established as a result of surgical removal of the lymph nodes of the neck, histological and histochemical study. Following the surgery, the child was discharged for further treatment at the department of oncohematology.

Keywords

• Rosai — Dorfman disease
• histiocytosis
• children.