Prune belly syndrome with urethral hypoplasia and vesico-cutaneous fistula: A case report and review of literature

Abstract

Association between Prune belly syndrome (PBS) and urethral hypoplasia is an unusual condition. It is usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with urethral hypoplasia and congenital vesico-cutaneous fistula in a male neonate. Patient underwent cutaneous vesicostomy and was discharged for close follow up of his renal function and for future reconstruction.

Keywords

• Prune belly syndrome
• urethral hypoplasia
• vesico-cutaneous fistula
• vesicostomy