Pulmonary Involvement at Connective Tissue Systemic Diseases in Children

Abstract

Pulmonary involvement in children with connective tissue systemic diseases is rare pathology that, however, has significant impact on treatment strategy and prognosis. This article presents data on the pulmonary involvement incidence, development, clinical features and results of visualization methods in children with such connective tissue systemic diseases as systemic sclerosis, juvenile dermatomyositis, systemic lupus erythematosus, and Sjogren’s syndrome. The issues of pathogenesis, risk factors of lung damage, therapeutic approaches and prognosis are considered.

Keywords

• системная склеродермия с ювенильным началом
• ювенильный дерматомиозит
• системная красная волчанка с ювенильным началом
• синдром шегрена у детей
• интерстициальное поражение легких
• легочная артериальная гипертензия