Interdisciplinary Neurosurgery (Sep 2020)

Cystic meningioangiomatosis in a middle-aged male patient: Case report and literature review

  • Long Chen,
  • Pengju Sun,
  • Clara Starkweather,
  • Robert M. Koffie,
  • Miaojing Fan,
  • Siyang Zhu,
  • Zhibo Gao

Journal volume & issue
Vol. 21
p. 100714

Abstract

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Meningioangiomatosis (MA) is a clinically rare intracranial lesion that occurs sporadically or develops as a component of neurofibromatosis-2 (NF-2). MA can present as either solid or cystic lesions. Cystic MA is extremely rare, with no specific manifestations on imaging, but can present clinically as a seizure inciting focus. We report a rare case of cystic MA that presented as intractable epilepsy. The patient was a 47-year-old male construction worker with no history of genetically predisposing disorders. Magnetic resonance imaging (MRI) showed a circular and well-defined, low-density lesion in the right temporal lobe, with an enhancing mural nodule. Surgical resection was performed, and histologic pathology confirmed MA. We review the literature on identification, diagnosis, and management strategies for MA.

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