JACC: Case Reports (Aug 2020)

A Long-Term Survivor With Alveolar Capillary Dysplasia

  • Chandler E. Yost, BS,
  • Angelica R. Putnam, MD,
  • Megan K. Dishop, MD,
  • Lynda O. Jorgensen, RN,
  • Paul E. Wirkus, MD,
  • Ronald W. Day, MD

Journal volume & issue
Vol. 2, no. 10
pp. 1492 – 1495

Abstract

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A patient with alveolar capillary dysplasia has survived more than 56 months with medical therapy. Intrauterine exposure to metformin potentially modified the severity of disease. In combination with other agents, endothelin receptor antagonists and amlodipine have been key medications in lowering pulmonary arterial pressure and managing right heart failure. (Level of Difficulty: Beginner.)

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