Mediterranean Journal of Hematology and Infectious Diseases (Aug 2014)

PRIMARY PANCREATIC LYMPHOMA IN A YOUNG PATIENT WITH EARLY ONSET TYPE I DIABETES MELLITUS

  • Valentina Bozzoli,
  • Francesco D'Alò,
  • Maria Chiara Tisi,
  • Giuseppina Massini,
  • Dario Pitocco,
  • Vittori Rufini,
  • Maria Lucia Calcagni,
  • Alberto Larghi,
  • Luigi Maria Larocca,
  • Luciana Teofili,
  • Stefan Hohaus

Journal volume & issue
Vol. 1

Abstract

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Primary pancreatic lymphoma (PPL) is an extremely rare disease which occurs in pancreas, and accounts for less than 1% of extra-nodal malignant lymphomas and 0,5% of cases of pancreatic masses. We report the case of PPL in a 15 year-old boy suffering from Type I Diabetes Mellitus (DM) diagnosed at the age of 1 year. The patient achieved complete remission by immuno-chemotherapy. An association between type I DM and PPL has never been reported so far and could represent a new link between chronic autoimmune disease and primary extranodal lymphoma in a target tissue.

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