Anaesthetic Management of a Patient with Arthrogryposis Multiplex Congenita: A Case Report

Abstract

Arthrogryposis multiplex congenita first described in 1905, is a rare congenital syndrome affecting 1 in 3000 births. It is characterized by multiple joint contractures found throughout the body and may be associated with multiple congenital anomalies like cleft palate, genitourinary defects, gastroschisis and cardiac defects. Hence appropriate evaluation should be done to rule out congenital abnormalities. Anaesthetic management may be complicated by difficult intravenous access, difficult positioning, difficult regional blockade and difficult airway. Anticipating difficulties and keeping alternate arrangements and preparation is required.

Keywords

• Arthrogryposis multiplex congenita
• anaesthesia
• anaesthetic management