Iatreia (Oct 2013)

Collapsing variant of focal segmental glomerulosclerosis in children = Variante colapsante de la glomeruloesclerosis focal y segmentaria en niños

  • Jonh Fredy Nieto Ríos,
  • Sandra Milena Brand,
  • Lina María Serna Higuita,
  • Luis Fernando Arias

Journal volume & issue
Vol. 26, no. 4
pp. 481 – 486

Abstract

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Focal segmental glomerulosclerosis (FSGS) collapsing variant refers to a renal lesion that may be idiopathic or associated to some factors, characterized by glomerular collapse leading to cortico-resistant nephrotic syndrome and chronic progressive renal failure. This glomerulopathy has been scarcely studied in children, but in this age group most cases are idiopathic. In this paper we present a report of 6 cases of collapsing variant of FSGS in children no associated to HIV, which were resistant to immunosuppressive management and with a high mortality

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