Emergencies in Hemophiliacs

Abstract

Audience: This modified team-based learning (mTBL) session is appropriate for medical students or emergency medicine residents. Introduction: Hemophilia is an x-linked recessive disorder leading to a decrease in functional clotting factors; there are two types, Hemophilia A and B, with deficiencies in clotting factors VIII and IX respectively. Patients are typically male and suffer from recurrent episodes of bleeding. The prevalence of hemophilia is low; therefore, many residents may not treat a patient with hemophilia during their training. Understanding the management and dosing of treatment factors is essential for emergency physicians. Objectives: By the end of this session learners will be able to: 1) describe the underlying deficiencies of hemophilia A and B; 2) discuss the complications of hemophilia; 3) formulate an appropriate treatment plan for an acutely bleeding hemophiliac; 4) calculate the appropriate factor dosing for a hemophiliac with acute bleeding. Method: The format of this education session is a modified TBL.

Keywords

• Hematology
• hemophilia
• bleeding emergencies
• hemorrhage