Journal of Dr. NTR University of Health Sciences (Jan 2020)
A case of Rasmussen's encephalitis with an atypical presentation
Abstract
Rasmussen's encephalitis (RE) is a chronic neurological disorder characterized by unilateral inflammation of the cerebral cortex leading to severe focal seizures, progressive loss of cognition, and neurological deficits in the affected hemisphere. We present a rare case of RE in a child with global developmental delay and cerebral atrophy. Neuroimaging helped in clinching the diagnosis of the disease. Immunomodulators may slow the progression of the disease; hence, it needs to be identified early and treated promptly. Functional cerebral hemispherectomy is the only treatment for drug-resistant seizures, but it has its functional compromise.
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