Extra-adrenal pheochromocytoma at the organ of Zuckerkandl: a case report and literature review

Abstract

Pheochromocytomas and paragangliomas are tumors that occur in characteristic locations and are commonly detected on imaging studies. A correct diagnosis is important because of differences in associated neoplasms, risk for malignancy, and need for genetic testing. In addition, associated complications, including death, can be avoided if appropriately recognized and treated. Here, we report a rare case of an extra-adrenal paraganglioma of the organ of Zuckerkandl.

Keywords

• Paraganglioma
• Pheochromocytoma
• Zuckerkandl
• Octreotide
• Neuroendocrine