Surgical treatment of congenital heart disease with Eisenmenger syndrome

Abstract

Article provides review of the available world literature on performing surgical correction of the atrioventricular septal defect (AVSD) in patients with Eisenmenger syndrome such as: basic pathophysiological principles, technique, indications, clinical and hemodynamic results. Currently, according to the literature, there is no clarity in the choice of a method for correcting severe congenital heart defects in combination with Eisenmenger syndrome (one - or two-step approach). The article presents the results of studies of both one-and two-stage approaches to correction of  the atrioventricular septal defect (AVSD) in this category of patients with their advantages and disadvantages.

Keywords

• atrioventricular septal defect
• pulmonary hypertension
• Eisenmenger syndrome
• Down syndrome.