Dancing eye syndrome: a case presentation

Abstract

Aim: To describe a case of a 14-month-old girl who presented to the eye clinic with unusual bouts of horizontal nystagmoid movements. Methods: The orthoptic findings are presented, along with the investigation results, underlying pathology, treatment and long-term prognosis. Results: A thoracic neuroblastoma was identified on chest X-ray and subsequent CT scan. After resection of the tumour the initial presenting sign of intermittent opsoclonus persisted. Conclusions: This case shows the presentation of an infant with dancing eye syndrome (DES), secondary to a thoracic neuroblastoma. Following the surgical resection of the primary tumour the intermittent opsoclonus remained. The ocular motility slowly returned to normal but some neurological sequelae persisted.

Keywords

• Ataxia
• Dancing eye syndrome (DES)
• Opsoclonus-myoclonus
• Thoracic neuroblastoma