We present a rare variant of pulmonary arteriovenous (AV) fistula (malformation), right pulmonary artery (RPA) to left atrium (LA) fistula, with its clinical and imaging findings with multidetector computed tomography (MDCT) pulmonary angiography and dynamic 3.0 T magnetic resonance imaging (MRI) pulmonary angiography in a 2-year-old female child who presented with central cyanosis at the age of 18 months.