Мать и дитя в Кузбассе (Aug 2020)

CONGENITAL MALFORMATION OF THE LIVER IN A NEWBORN (CLINICAL CASE)

  • Наталья Анатольевна Батина,
  • Лариса Георгиевна Кончевская,
  • Александр Владимирович Голомидов,
  • Вадим Гельевич Мозес,
  • Елена Владимировна Рудаева,
  • Светлана Ивановна Елгина,
  • Елена Германовна Рудаева

Journal volume & issue
Vol. 21, no. 3
pp. 78 – 81

Abstract

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Congenital hyperplasia of the intrahepatic bile ducts refers to early fetopathy. It represents a «bizarre» proliferation of bile ducts in the portal tract with excessive development of connective tissue. A frequent complication of this defect is the attachment of secondary purulent cholangitis. When combined with small cystic kidney disease, death occurs from renal failure in the first days of life.

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