CT of primary undifferentiated pleomorphic sarcoma of small intestine with distant metastases presenting with intussusception

Abstract

Undifferentiated pleomorphic sarcoma of bowel is very rare, only a few cases have been reported till date. A 29 year old male patient presented with acute abdominal pain due to intussusception, contrast enhanced computed tomography abdomen showed multiple endoluminal homogenously enhancing polypoidal lesions with distant metastasis. Radiologically our primary diagnosis was malignant gastrointestinal stromal tumor, however, histopathological evaluation turned out to be a small bowel undifferentiated pleomorphic sarcoma. Considering the multiplicity of lesion and early distant metastasis radiologist should also consider sarcoma involving bowel as one of the differential diagnosis. Keywords: Undifferentiated pleomorphic sarcoma (UPS), malignant fibrous histiocytoma (MFH), jejunojejunal intussusception and ileoileal intussusception