Педиатрическая фармакология (Sep 2019)
Distal Tubulopathy. Liddle Syndrome
- Alexander A. Baranov,
- Leyla S. Namazova-Baranova,
- Tatyana V. Sergeeva,
- Olga V. Chumakova,
- Svetlana S. Paunova,
- Nurali Z. Zokirov,
- Olga V. Komarova,
- Tea V. Margieva,
- Vladimir K. Tatochenko,
- Maya D. Bakradze,
- Elena N. Tsygina,
- Olga I. Zrobok,
- Tatiana V. Vashurina,
- Irina N. Lupan,
- Mikhail Yu. Kagan,
- Alexey N. Tsygin
Affiliations
- Alexander A. Baranov
- Central Clinical Hospital of the Russian Academy of Sciences
- Leyla S. Namazova-Baranova
- Central Clinical Hospital of the Russian Academy of Sciences; Pirogov Russian National Research Medical University
- Tatyana V. Sergeeva
- National Medical Research Center of Children's Health
- Olga V. Chumakova
- National Medical Research Center of Children's Health
- Svetlana S. Paunova
- National Medical Research Center of Children's Health
- Nurali Z. Zokirov
- The Central Pediatric Clinical Hospital of FMBA of Russia
- Olga V. Komarova
- National Medical Research Center of Children's Health
- Tea V. Margieva
- Central Clinical Hospital of the Russian Academy of Sciences
- Vladimir K. Tatochenko
- National Medical Research Center of Children's Health
- Maya D. Bakradze
- National Medical Research Center of Children's Health
- Elena N. Tsygina
- National Medical Research Center of Children's Health
- Olga I. Zrobok
- National Medical Research Center of Children's Health
- Tatiana V. Vashurina
- National Medical Research Center of Children's Health
- Irina N. Lupan
- South Ural State Medical University
- Mikhail Yu. Kagan
- Regional Children's Clinical Hospital
- Alexey N. Tsygin
- National Medical Research Center of Children's Health
- DOI
- https://doi.org/10.15690/pf.v16i3.2026
- Journal volume & issue
-
Vol. 16,
no. 3
pp. 149 – 151
Abstract
The clinical recommendations on management of children with Liddle syndrome which is characterized by severe hypertension along with low activity levels of renin and aldosterone in blood plasma, hypokalemia and metabolic alkalosis, were developed by the experts of the Union of pediatricians of Russia. Aspects of epidemiology, etiology and pathogenesis, disease progression, differential diagnostics and evidence-based treatment are presented.
Keywords
