Plastic and Reconstructive Surgery, Global Open (Aug 2023)

A Rare Giant Nasofrontal Meningoencephalocele with Nasal and Visual Obstruction

  • Celso A. Aldana, MD, PhD,
  • Carlos Gimenez, MD,
  • Orlando Avalos, MD,
  • Elvio Mendez, MD,
  • Adriana Peña, MD,
  • Pablo Ramirez, MD,
  • Jesus Amarilla, MD,
  • Dulce Añazco, MD,
  • Jose Sandoval, MD

DOI
https://doi.org/10.1097/GOX.0000000000005215
Journal volume & issue
Vol. 11, no. 8
p. e5215

Abstract

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Summary:. The encephalocele is a malformation that is manifested by the protrusion of brain tissue through a defect in the skull. The meningoencephalocele contains the meninges and brain tissue. Frontoethmoidal or nasal meningoencephalocele is rare; the frequency is approximately one in 40,000 live births. Three subtypes are currently known: nasoethmoid, nasofrontal, and nasoorbital. The authors report the clinical case of a 2-month-old girl with a very rare giant nasofrontal meningoencephalocele, which affected vision and breathing. The patient underwent surgery at an early age to avoid significant functional sequelae and promote the normal development and growth of the girl.