Case Reports in Dermatological Medicine (Jan 2014)

Dyschromatosis Symmetrica Hereditaria of Late Onset?

  • Caroline Balvedi Gaiewski,
  • Sergio Zuneda Serafini,
  • Betina Werner,
  • Janyana M. D. Deonizio

DOI
https://doi.org/10.1155/2014/639537
Journal volume & issue
Vol. 2014

Abstract

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Dyschromatosis symmetrica hereditaria (DSH), also known as reticulated acropigmentation of Dohi, is an autosomal dominant disease with high penetrance, characterized by hypo- and hyperpigmented macules of varying sizes on the dorsal of the extremities with reticulated pattern. This paper presents a female patient with typical dermatological lesions, but only diagnosed in adulthood. It is necessary to perform differential diagnosis with other pigmentary disorders. This entity is not very common in South America, and the vast majority of cases were described in Japanese population. Since it is a benign disease, it is important to be aware of this diagnosis in order to establish the correct conduct for these patients.