Radiology Case Reports (Mar 2023)

A rare case of left atrial myxofibromyosarcoma

  • Pallavi Srivastava, MBBS, MPH,
  • Fabricio Feltrin, MD,
  • Vishal Kukkar, MD

Journal volume & issue
Vol. 18, no. 3
pp. 771 – 774

Abstract

Read online

Myxofibrosarcoma is an aggressive soft tissue sarcoma, previously known as myxoid variant of malignant fibrous histiocytoma. Primary cardiac myxofibrosarcomas are the rarest forms of cardiac malignant tumors that often remain asymptomatic until metastasis occurs. In this case report, we describe a rare left atrial cardiac myxofibrosarcoma in a patient with recurrent renal cell carcinoma. We discuss the multimodality imaging approach to diagnose and evaluate cardiac masses as well as imaging characteristics to differentiate cardiac masses from thrombus.

Keywords