Perioperative anaesthesia management in a parturient with arthrogryposis multiplex congenital posted for caesarean delivery

Abstract

Arthrogryposis multiplex congenital is usually associated with multiple congenital abnormalities, including skeletal deformities, congenital heart disease and sometimes alterations of the respiratory and genitourinary systems. Challenges faced by the anesthesiologist when dealing with patients with this syndrome include potential difficult airway, risk of malignant hyperthermia associated with myopathy, cardiorespiratory problems, difficult regional blockade, difficult IV access, and difficult positioning. Hence these patients need meticulous care perioperatively. Though regional anaesthesia is technically challenging in them, it has been used successfully in them.

Keywords

• arthrogryposis multiplex congenita
• caesarean delivery
• regional anaesthesia