Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome

Abstract

Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler–Danlos syndrome. Loeys–Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation.

Keywords

• aortic aneurysm
• bentall procedure
• loeys–dietz syndrome