Neuropsychological rehabilitation in people with Prader-Willi syndrome

Abstract

Prader-Willi Syndrome (PWS) is a complex neurodevelopmental disorder caused by genetic anomalies that presents itself with a characteristic neurobehavioral phenotype. The aim of this project was to analyze interventions of neuropsychological rehabilitation that exist in PWS and to achieve it, a systematic search was done, resulting in a total of 14 articles with interventions for behavioral, cognitive and familial phenotypical characteristics. The studies were analyzed according to the focus of the intervention, models, specific procedures and results. Most studies used a compensation model and almost all applied behavioral modification techniques. The results suggest that techniques that use differential reinforcement and a more active involvement of the person with PWS and their family during intervention, are more successful.

Keywords

• síndrome de prader-willi
• fenotipo conductual
• rehabilitación
• neuropsicología.