An Interesting Association with Pulmonary Hypertension: Swyer-James-Macleod Syndrome

Abstract

Pulmonary hypertension (PH) is a chronic disease that has increased awareness in recent years and has high morbidity and mortality. There are many unexplained points outside the current PH classification. Congenital heart diseases and lung pathologies are important causes of PH. Swyer-James-Macleod syndrome is a syndrome characterized by unilateral pulmonary arterial flow reduction due to involvement mostly in childhood and contralateral lung hyperlucency in imaging methods. It is rare for this syndrome to be observed together with congenital heart diseases and to be defined in a patient with PH.

Keywords

• atrial septal defect
• congenital heart disease
• pulmonary hypertension
• swyer-james-macleod syndrome