Anais Brasileiros de Dermatologia (Jun 2018)

Nasal-type extranodal T-cell/NK lymphoma in association with hemophagocytic syndrome

  • Juliana Chaves Ruiz Guedes,
  • Karen de Almeida Pinto Fernandes da Cunha,
  • Jorge Ricardo da Silva Machado,
  • Luciana Wernersbach Pinto

DOI
https://doi.org/10.1590/abd1806-4841.20187097
Journal volume & issue
Vol. 93, no. 3
pp. 422 – 425

Abstract

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Abstract: Extranodal NK/T-cell lymphoma nasal type is a rare disease that mainly affects the nasal cavity and paranasal sinuses of males in the fifth decade of life. It has aggressive and locally destructive behaviour, and can be complicated by the hemophagocytic syndrome, conferring high lethality to the disease. This article describes a case of NK/T-cell lymphoma nasal type in a previously healthy patient, exemplifying its rapid and fulminant course.

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