Orthognathic surgery in a patient with osteopathia striata combined with cranial sclerosis: A case report

Abstract

Osteopathia striata combined with cranial sclerosis (OSCS) is a skeletal dysplasia, characterized by linear striation in the long bones and cranial osteosclerosis. OSCS leads to various abnormalities in the cranial and facial bones and disfigurements, including dental arch discrepancies. Here, we present a case of OSCS where dental arch discrepancies were corrected with bimaxillary orthognathic surgery. Boney sclerosis leads to an increase in bone density that can cause complications during and after surgery. Therefore, it is important to evaluate these patients thoroughly with cone beam computed tomography before performing surgery. Analyze of previous surgical procedures as well as adaptation of the surgical technique to the hard brittle bone must take place.

Keywords

• OSCS
• Dental arch discrepancies
• Bimaxillary orthognathic surgery
• Bone healing