Kyphoscoliosis caused by lymphangiogenic form of Gorham – Stout disease with axial skeletal lesion

Abstract

The paper presents a clinical observation of a child with lymphangiogenic form of spontaneous osteolysis (Gorham – Stout disease) associated with massive destruction of the rib cage and progressive kyphoscoliotic deformity. Staged surgical treatment under the therapy with osteoclast inhibitors resulted in the deformity correction and significant improvement in the quality of life. The prognosis remains unclear due to the risk of osteolysis progression.

Keywords

• spontaneous osteolysis
• children
• gorham-stout disease
• gsd
• hylothorax
• kyphoscoliosis
• osteoclast inhibitors