Aggressive fibromatosis of the oral cavity in a 5 year old boy: a rare case report

Abstract

Fibrous tissue proliferations express a wide spectrum of histologic and morphologic variations in both infants and adults. This ranges from hypertrophic scar formation at one end to malignant fibrosarcoma at the other end of the spectrum. Aggressive fibromatosis is an intermediate tumour which is in proximity to fibro sarcomas. These are locally invasive and often recur after excision, but do not metastasize. Histologically, they are characterized by proliferating fibroblasts with little mitotic activity. Aggressive fibromatosis in the head and neck region is not common, and very sporadically occurs in the oral cavity or jaw bones. Here we report a rare case of aggressive fibromatosis occurring in a 5 year old boy.

Keywords

• aggressive fibromatosis
• desmoid tumor
• infantile fibromatosis
• soft tissue tumour
• extra abdominal fibromatosis