A Rare Cardiac Anomaly in Absent Pulmonary Valve Syndrome with Tetralogy of Fallot

Abstract

Heart failure and cardiomegaly are observed in patients with absent pulmonary valve syndrome with tetralogy of Fallot (TOF), unlike in those with TOF alone. Additional cardiac anomalies can also be seen in these patients, although not frequently. In our case, we found that the right and left pulmonary arteries were disconnected (the main pulmonary artery continued only with the right pulmonary artery and the left pulmonary artery originating from patent ductus arteriosus). In this paper, we wanted to remember other cardiac anomalies associated with absent pulmonary valve syndrome with tetralogy of Fallot.

Keywords

• Absent pulmonary valve
• tetralogi of Fallot
• patent ductus arteriosus
• non-confluent pulmonary arteries