The Report of a Very Rare Case of Peseudoxanthomatous Mastocytosis

Abstract

Diffuse cutaneous mastocytosis is very rare variety mast-cell disorder which is called peseudoxanthomatous mastocytosis. Our case was a man who was eighteen years old. He suffered from yellow papules on the neck, extremities , axillary and groins. The appearance of large blisters following mild trauma or occuring spontaneously. Our patients Pruritus was not very server. The examination of his skin revealed yellow boggy and thickened skin with a doughy consistency without systemic involvement. Considering the clinical signs and using the skin biopsy reports of the patient, the illness was diagnosed as peseudoxanthomatous mastocytosis.

Keywords

• urticaria pigmentosa–diagnosis /urticaria pigmentosa–pathology