Cancers (Jun 2023)
Updated Review and Clinical Recommendations for the Diagnosis and Treatment of Patients with Retroperitoneal Sarcoma by the Spanish Sarcoma Research Group (GEIS)
- Rosa Álvarez Álvarez,
- Aránzazu Manzano,
- Carolina Agra Pujol,
- Vicente Artigas Raventós,
- Raquel Correa,
- Josefina Cruz Jurado,
- Juan Angel Fernandez,
- Xavier Garcia del Muro,
- Jose Antonio Gonzalez,
- Nadia Hindi,
- Pablo Lozano Lominchar,
- Javier Martínez-Trufero,
- Ramiro Méndez,
- Mercedes Muñoz,
- Cristobal Muñoz Casares,
- Francisco Orbis Castellanos,
- Ruth Orellana Fernandez,
- Miguel Paniagua González,
- Andres Redondo,
- Claudia Valverde Morales,
- Jose Manuel Asencio
Affiliations
- Rosa Álvarez Álvarez
- Medical Oncology Department, Instituto de Investigacion Sanitaria Gregorio Marañon, Hospital Universitario Gregorio Marañon, 28007 Madrid, Spain
- Aránzazu Manzano
- Medical Oncology Department, Hospital Universitario Clínico San Carlos, 28040 Madrid, Spain
- Carolina Agra Pujol
- Pathology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain
- Vicente Artigas Raventós
- Surgery Department, Hospital Universitario Sant Pau, Universidad Autonoma de Barcelona, 08035 Barcelona, Spain
- Raquel Correa
- Radiation Oncology Department, Hospital Virgen de la Victoria, 29010 Malaga, Spain
- Josefina Cruz Jurado
- Medical Oncology Department, Hospital Universitario Canarias, 38320 Santa Cruz de Tenerife, Spain
- Juan Angel Fernandez
- Sarcoma Multidisciplinary Unit, Surgery Department, Hospital Virgen de la Arrixaca, 30120 Murcia, Spain
- Xavier Garcia del Muro
- Sarcoma Multidisciplinary Unit, Medical Oncology Department, Idibell, Instituto Catalan Oncología Hospitalet, 08908 Barcelona, Spain
- Jose Antonio Gonzalez
- Surgery Department, Hospital Universitario Sant Pau, Universidad Autonoma de Barcelona, 08035 Barcelona, Spain
- Nadia Hindi
- Medical Oncology Department, Fundacion Jimenez Diaz University Hospital, 28040 Madrid, Spain
- Pablo Lozano Lominchar
- Surgery Department, Hospital Universitario Gregorio Marañon, Complutense University, 28040 Madrid, Spain
- Javier Martínez-Trufero
- Medical Oncology Department, Hospital Universitario Miguel Servet, 50009 Zaragoza, Spain
- Ramiro Méndez
- Radiology Department, Hospital Universitario Clínico San Carlos, 28040 Madrid, Spain
- Mercedes Muñoz
- Radiation Oncology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain
- Cristobal Muñoz Casares
- Surgery Department, Hospital San Juan de Dios, 14012 Cordoba, Spain
- Francisco Orbis Castellanos
- Sarcoma Multidisciplinary Unit, Surgery Department, Hospital Universitario y Politécnico La Fe, 46026 Valencia, Spain
- Ruth Orellana Fernandez
- Pathology Department, Hospital Universitario Santa Creu i Sant Pau, 08025 Barcelona, Spain
- Miguel Paniagua González
- Radiology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain
- Andres Redondo
- Medical Oncology Department, Hospital Universitario La Paz—IdiPAZ, 28046 Madrid, Spain
- Claudia Valverde Morales
- Medical Oncology Department, Vall D’Hebron University Hospital, 08035 Barcelona, Spain
- Jose Manuel Asencio
- Surgery Department, Hospital Universitario Gregorio Marañon, Complutense University, 28040 Madrid, Spain
- DOI
- https://doi.org/10.3390/cancers15123194
- Journal volume & issue
-
Vol. 15,
no. 12
p. 3194
Abstract
Soft tissue sarcomas (STS) are an uncommon and biologically heterogeneous group of tumors arising from mesenchymal cells. The incidence is estimated at five cases per 100,000 people per year. Retroperitoneal sarcomas (RPS) account for 10–15% of all STS, and their management depends on their anatomical characteristics and histotype. Due to their very low incidence, it is recommended that RPS be treated in reference centers and evaluated by an experienced multidisciplinary team (MDT). In Spain, the Spanish Group for Research in Sarcomas (GEIS) brings together experts from various specialties to promote research on sarcomas and improve treatment results. This paper summarizes the GEIS recommendations for the diagnosis, treatment, and follow-up of patients with RPS.
Keywords
- retroperitoneal sarcoma
- soft tissue sarcoma
- retroperitoneum
- multidisciplinary board
- reference centers