Management of a Case of von Hippel-Lindau for Coronary Artery Bypass Grafting

Abstract

von Hippel-Lindau (VHL) disease is a rare autosomal dominant genetic disorder with retinal and nervous system haemangioblastomas, phaeochromocytoma, renal, pancreatic and endolymphatic tumours. These patients usually present for surgeries involving cerebellar or adrenal tumours. In this article, intraoperative management of a case of VHL, operated for coronary artery bypass grafting is discussed.

Keywords

• von Hippel-Lindau disease
• coronary artery bypass grafting
• renal cell carcinoma
• pheochromocytoma
• hypertension