Giant dermatofibrosarcoma protuberans on the abdominal wall

Abstract

Dermatofibrosarcoma protuberans is probably best considered as alow-grade dermal sarcoma. It is an uncommon type of sarcoma thatmay occur anywhere in the body. It rarely arises on the abdominal wall.It often affects young patients and appears as a nodular mass. Thegrowth pattern is usually slow and persistent. These lesions enlargeover many years, becoming protuberant. These tumors have a locallyaggressive nature and may recur frequently. They rarely metastasize.A wide resection with 2-3 cm free margins is the best treatment. Thispaper reports a rare type of abdominal wall sarcoma. A brief literaturereview is presented showing the surgical principles for treatingabdominal wall tumors and their outcome. Radical surgery and goodlocoregional control are shown to be significantly related.

Keywords

• Dermatofibrosarcoma
• Abdominal wall/pathology
• Soft tissue neoplasms