Total anomalous systemic venous drainage to the left atrium: An entity reviewed and investigated

Abstract

We present three unusual cases of total anomalous systemic venous drainage (TASVD) where all the systemic veins were abnormally connected to the atrium that drained into the left ventricle (LV). All three patients had features consistent with left atrial isomerism. Based on the available evidence and review of literature we propose that TASVD be included as a part of the syndrome of left atrial isomerism. A classification for TASVD is also proposed with surgical implications.

Keywords

• Heterotaxy syndrome
• left isomerism
• total anomalous systemic venous drainage