Under Pressure: A Case of Developmental Glaucoma and Congenital Glaucoma in Sturge–Weber Syndrome

Abstract

Sturge–Weber syndrome (SWS), also known as encephalo-trigeminal angiomatosis, is a sporadic, congenital neurocutaneous disorder. It is characterized by capillary malformation affecting the brain, meninges, eyes, and skin. The ophthalmic, maxillary, and mandibular distributions of the trigeminal nerve are involved. Eye involvement with vascular malformation produces glaucoma and can lead to vision loss. Here, we present a rare case of SWS with port-wine stain, painful vision loss in left eye, and open-angle glaucoma in the other eye of the same patient. The painful blind eye was treated with cyclocryotherapy with successful control of intraocular pressure.

Keywords

• congenital glaucoma
• cyclocryotherapy
• sturge–weber syndrome