Successful Weaning of a Laryngeal Mask Airway After a Tongue-lip Adhesion Operation in a Case With Cerebro-costo-mandibular Syndrome

Abstract

Cerebro-costo-mandibular syndrome (CCMS) consists of severe micrognathia, glossoptosis, posterior rib-gap defects and developmental delay. It may cause upper airway obstruction and flail chest, resulting in neonatal hypoxia, and possibly death. Early airway management or surgical intervention to maintain a patent airway is critical to avoid hypoxia in CCMS patients. We report a newborn with CCMS who was successfully weaned from a laryngeal mask after undergoing a tongue–lip adhesion operation at 164 days of age.

Keywords

• airway obstruction
• cerebro-costo-mandibular syndrome
• tongue-lip adhesion