Pachydermoperiostosis as a Rare Cause of Blepharoptosis

Abstract

A 37-year-old male patient diagnosed with pachydermoperiostosis at another center came to our clinic to rectify his blepharoptosis. The physical examination of the patient revealed skeleton and skin symptoms typical for pachydermoperiostosis. There was thickening and extending horizontal length of the eyelids, an S-shaped deformity on the edges of the eyelids, and symmetric bilateral mechanical blepharoptosis. In order to treat the blepharoptosis, excision of the thickened skin and the orbicular muscle as well as levator aponeurosis surgery was performed. The esthetic result was satisfactory. Pachydermoperiostosis is a rare cause of blepharoptosis. Meibomius gland hyperplasia, increase of collagen substance in the dermis, mucin accumulation are reasons of thickening the eyelid and finally this causes the development of mecanical blepharoptosis. Even though many two or three phased surgical procedures can be applied to these cases, satisfactory results can be achieved with levator surgery and excision of the thickened skin and the orbicular muscle as well. (Turk J Ophthalmol 2014; 44: 416-8)

Keywords

• Pachydermoperiostosis
• primary hypertrophic osteoarthropathy
• ptosis