Рациональная фармакотерапия в кардиологии (Jul 2017)

ANGIOSARCOMA OF THE HEART – CLINICAL CASE

  • N. Yu. Karpova,
  • M. A. Rashid,
  • T. V. Kazakova,
  • N. S. Chipigina,
  • A. V. Aksenova,
  • R. V. Ershov,
  • Zh. I. Banova,
  • E. M. Levin,
  • A. A. Byshov,
  • B. V. Uvarovskaya

DOI
https://doi.org/10.20996/1819-6446-2017-13-3-339-345
Journal volume & issue
Vol. 13, no. 3
pp. 339 – 345

Abstract

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Primary angiosarcoma of the heart, constituting 33% of primary heart malignancies in adults, refers to rare diseases with a difficult diagnosis. The article describes the case of primary angiosarcoma of the right atrium, diagnosed posthumously in a patient of 45 years old. The disease debuted in a previously healthy woman 45 years, 2 months before her death. There were episodes of sudden decrease in blood pressure with pain in the chest and short-term loss of consciousness, as well as moderate manifestations of heart failure (hydrothorax, small ascites, hydropericardium, hepatomegaly, leg shunting). The patient died suddenly, a pathologic study revealed an angiosarcoma of the right atrium with invasive growth, accompanied by inferior vena cava stenosis. Angiosarcoma of the heart should be included in a differential diagnosis of patient with pericardial effusion of unspecified genesis, syndromes of vena cava obstruction, unexplained right ventricular failure, syncope with a fall in blood pressure, especially in middle-aged patients.

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