Melanotic neuroectodermal tumor of infancy: a rare presentation of an extremely rare neoplasm and diagnostic implications in Gombe, Nigeria

Abstract

Melanotic neuro-ectodermal tumor of infancy is very rare. A unique neoplasm of the formative years, it typically involves the face or cranium; possesses rapid, expansile growth; presents as a firm swelling and displays a high rate of recurrence. Its rarity and unique features make diagnosis and management quite challenging. This challenge is increased in resource-limited settings like ours and with atypical presentation, such as was seen at our center, where patient presented with a bony hard swelling.

Keywords

• melanotic neuro-ectodermal tumor of infancy
• benign tumor
• maxillary tumor
• infant
• bony-hard swelling
• firm swelling
• diagnostic challenges
• management challenges
• vanyl mandellic acid
• wide excision