Idiopathic pulmonary fibrosis: a clinical case of long-term follow-up

Abstract

Idiopathic pulmonary fibrosis is a specific form of chronic progressive fibrotic interstitial pneumonia of unknown etiology. Over the past decade, significant progress has been made in developing and utilizing a diagnostic algorithm for patients with idiopathic pulmonary fibrosis, involving analysis of clinical, laboratory, and instrumental data, primarily the results of high-resolution chest computed tomography. Early antifibrotic therapy can alter the disease course, slow its progression, and improve the prognosis.

Keywords

• idiopathic pulmonary fibrosis
• antifibrotic therapy
• pirfenidone
• clinical case